Hemoglobin Duarte : ( a 2 fl

نویسنده

  • H. Lehmann
چکیده

A patient with a normal blood hemoglobin was found to be heterozygous for a new level, but with evidence of brisk hemolfl-chain mutation and fl-thalassemia. All ysis, was found to have an unstable of the hemoglobin in his red cells was of hemoglobin with a left-shifted oxygen the abnormal type, designated hemodissociation curve. Two sisters of the paglobin Duarte, and was shown to contain tient had a history of hemolytic anemia. proline at the $62 (E6) position instead of Both died of thromboembolic complicaalanine. tions following splenectomy. Our patient

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تاریخ انتشار 2005